Variant Details

Variant Selected: c.541C>T; p.R181C


Variant Description


Genomic Description (hg38) cDNA Description Protein Description Exon nb CpG Site Splice Site Sequence Context WT Codon Mutant Codon Effect Effect Group3
g.7675071G>A c.541C>T p.R181C 5-exon yes no G_G CGC TGC missense 1

Predicted or Observed Splicing Effects on Main Transcript


Site Type p53Site WT Score MUT Score Variation Source
- no significant change NNSPLICE 0.9

SpliceAI Predictions on Canonical Transcript (NM_000546.5) by Jaganathan (2019) [ GitHub]


Delta Score_AG Delta Score_AL Delta Score_DG Delta Score_DL Delta Position_AG Delta Position_AL Delta Position_DG Delta Position_DL
0 0.01 0.03 0 997 -117 28 265

Protein Features


Structural Motif Domain Function Residue Function Cancer Hotspot Variant Rate SwissProt
L2/L3 DNA binding Exposed yes 1.28 044946

Systematic Assessment of Transactivation Capacities in Yeast and Saos2 Assays by Kato (2003) and Kakudo (2005)


WAF1 MDM2 BAX H1433s AIP1 GADD45 NOXA P53R2 WAF1 (Saos2) MDM2 (Saos2) BAX (Saos2) h1433s (Saos2) AIP1 (Saos2) PUMA (Saos2)
43.1 21.7 18.6 9.4 21.0 51.3 70.2 128.0

Predicted or Observed Impacts on Protein Functions


Transactivation Class DNE DNE_LOF Class Align-GVGD BayesDel REVEL SIFT Polyphen2 Structure Function
partially functional Moderate notDNE_notLOF C65 0.4693 0.891 Damaging D functional

Predicted Effect on p53 Protein Isoforms


TAp53 Alpha TAp53 Beta TAp53 Gamma Delta40p53 Alpha Delta40p53 Beta Delta40p53 Gamma Delta133p53 Alpha Delta133p53 Beta Delta133p53 Gamma Deltap53 Alpha
Altered Altered Altered Altered Altered Altered Altered Altered Altered Altered

Various Activities Assessed in Yeast or Human Assays


Lost Function Retained Function Gain of Function Dominant Negative Activity Temperature Sensitivity Cell Lines PubMed
TRANSF- NA TRANSF+ (moderate) NA NA REF 10229196
NA GS (in vitro) NA NA NA H1299 29979965
TA (WAF1 5') partial; TA (WAF1 3', P53R2, GADD45, CD95-Fas, 14-3-3s, PCNA, AIP1, MDM2, MDM2-RE2, RGC, IGF-BP3, PA26, BAX) NA NA Yes [TA (IGF-BP3, WAF1 3', NOXA, PUMA)] moderate NA Yeast 12909720
TA (MDM2, BAX, PUMA); TA (WAF1) partial NA NA Yes [TA (MDM2, BAX)]; No [TA (PUMA, WAF1)] NA Yeast 21343334
NA NA NA Yes [TA (BAX)]; No [TA (WAF1 5’, PIG3)] NA Yeast 11896595
TA (RGC) NA p73beta interference NA NA Yeast 12917626
Upregulation (p21waf1) partial; TA (MDM2, BAX, IGF-BP3-boxA) TA (WAF1, PIG3); GS; APO NA NA NA Saos-2 10229196

Mouse Models Engineered with the Selected Mutant


No Data

Experimentally Induced Variants


Exposure Model PubMed
B(a)P-7,8-dione Yeast reporter gene assay 23117049
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